Paediatric Surgery and Urology, Institute for Maternal and Child Health - IRCCS "Burlo Garofolo", Trieste, Italy,
Hernia. 2014 Jun;18(3):417-21. doi: 10.1007/s10029-012-1042-y. Epub 2013 Jan 17.
Hepatic pulmonary fusion is a rare malformation associated with right congenital diaphragmatic hernia (CDH), often only discovered during surgical repair of the defect. Fourteen previous cases have been reported in the literature. We describe a case of a full term male newborn with prenatal ultrasound diagnosis of right CDH who underwent a thoracoscopy converted to a thoracotomy, due to this rare aforementioned intraoperative incidental finding. We reviewed the previous reported literature, especially focusing on the chosen surgical approach, concluding that an early and appropriate preoperative imaging investigation may be crucial for the best management of these kinds of patients.
肝肺融合是一种罕见的畸形,与右侧先天性膈疝(CDH)有关,通常仅在手术修复缺陷时发现。文献中已有 14 例报道。我们描述了一例足月男性新生儿,产前超声诊断为右侧 CDH,因术中发现上述罕见的意外情况,改行胸腔镜检查转为开胸手术。我们回顾了以往报道的文献,特别是重点关注了所选的手术方法,得出结论:早期和适当的术前影像学检查对于这类患者的最佳治疗可能至关重要。