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腹膜后囊性淋巴管瘤:诊断与手术挑战

Retroperitoneal cystic lymphangioma: a diagnostic and surgical challenge.

作者信息

Gümüştaş Oguzhan Güven, Sanal Murat, Güner Osman, Tümay Volkan

机构信息

Department of Radiology, Acıbadem Bursa Hospital, FSM Street, 16110 Bursa, Turkey.

出版信息

Case Rep Pediatr. 2013;2013:292053. doi: 10.1155/2013/292053. Epub 2013 Feb 28.

Abstract

A lymphangioma is a benign proliferation of lymph vessels, producing fluid-filled cysts that result from a blockage of the lymphatic system. The incidence of abdominal lymphangiomas is unknown; however they account for from 3% to 9.2% of all pediatric lymphangiomas, with retroperitoneal lymphangioma representing less than 1% of abdominal lymphangiomas. Due to rarity, preoperative diagnosis is often difficult.

摘要

淋巴管瘤是淋巴管的良性增殖,产生因淋巴系统阻塞而形成的充满液体的囊肿。腹部淋巴管瘤的发病率尚不清楚;然而,它们占所有小儿淋巴管瘤的3%至9.2%,其中腹膜后淋巴管瘤占腹部淋巴管瘤的比例不到1%。由于其罕见性,术前诊断往往很困难。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6018/3600274/77a13dff02aa/CRIM.PEDIATRICS2013-292053.001.jpg

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