Bhavsar Tapan, Saeed-Vafa Daryoush, Harbison Sean, Inniss Susan
Tapan Bhavsar, Daryoush Saeed-Vafa, Susan Inniss, Department of Pathology and Laboratory Medicine, Temple University Hospital, Philadelphia, PA 19140, United States.
World J Gastrointest Pathophysiol. 2010 Dec 15;1(5):171-6. doi: 10.4291/wjgp.v1.i5.171.
Lymphangiomas are rare benign cystic tumors of the lymphatic system. Retroperitoneal lymphangiomas account for 1% of all lymphangiomas, and approximately 186 cases have been reported. They may clinically present as a palpable abdominal mass and can cause diagnostic dilemmas with other retroperitoneal cystic tumors, including those arising from the liver, kidney and pancreas. This report describes the rare case of a cystic retroperitoneal lymphangioma in a 54-year-old male patient. The lymphangioma had progressed to the point of inducing clinical symptoms of abdominal distention, abdominal pain, anorexia, fever, nausea and diarrhea. Radiological imaging revealed a large multiloculated cystic abdominal mass with enhancing septations involving the upper retroperitoneum and extending into the pelvis. Surgical removal of the cyst was accomplished without incident. A benign cystic retroperitoneal lymphangioma was diagnosed on histology and confirmed with immunohistochemical stains.
淋巴管瘤是淋巴系统罕见的良性囊性肿瘤。腹膜后淋巴管瘤占所有淋巴管瘤的1%，已报道约186例。临床上，它们可能表现为可触及的腹部肿块，并且可能与其他腹膜后囊性肿瘤（包括源自肝脏、肾脏和胰腺的肿瘤）导致诊断难题。本报告描述了一名54岁男性患者发生囊性腹膜后淋巴管瘤的罕见病例。该淋巴管瘤已发展到引起腹胀、腹痛、厌食、发热、恶心和腹泻等临床症状的程度。放射影像学显示一个巨大的多房性囊性腹部肿块，伴有强化的分隔，累及上腹膜后并延伸至盆腔。囊肿的手术切除顺利完成。组织学诊断为良性囊性腹膜后淋巴管瘤，并经免疫组化染色证实。
