Maa John, Wa Christianne, Jaigirdir Adnan, Cho Soo-Jin, Corvera Carlos U
Department of Surgery, University of California;
Rare Tumors. 2009 Dec 28;1(2):e48. doi: 10.4081/rt.2009.e48.
Lymphangiomas are congenital malformations of the lymphatic system that account for about 5% of all benign tumors in infants and children.(1) The most common sites are the neck and axilla, which account for 95% of cases.(2) Abdominal cystic lymphangiomas are quite rare, and can arise from either the retroperitoneum, gastrointestinal tract, or the mesentery of the abdominal viscera.(3) The presenting symptoms are painless abdominal distension, a palpable mass, or secondary complications in the abdomen such as intestinal obstruction, volvulus, intestinal infarction, or bleeding.(4) Typically diagnosed during childhood, these tumors prompt surgical intervention. We describe an atypical case of an abdominal cystic lymphangioma, which did not manifest until adulthood, with atypical symptoms of a rapidly expanding and symptomatic mass.
淋巴管瘤是淋巴系统的先天性畸形，约占婴幼儿所有良性肿瘤的5%。（1）最常见的部位是颈部和腋窝，占病例的95%。（2）腹部囊性淋巴管瘤相当罕见，可起源于腹膜后、胃肠道或腹腔内脏器的肠系膜。（3）表现症状为无痛性腹胀、可触及的肿块，或腹部的继发性并发症，如肠梗阻、肠扭转、肠梗死或出血。（4）这些肿瘤通常在儿童期被诊断出来，并促使进行手术干预。我们描述了一例非典型的腹部囊性淋巴管瘤病例，该病例直到成年才出现，伴有快速增大且有症状的肿块的非典型症状。
