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Adult-onset leukoencephalopathy with axonal spheroids and pigmented glia can present as frontotemporal dementia syndrome.成人起病伴轴索性球体和色素性神经胶质的脑白质病可表现为额颞叶痴呆综合征。
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临床推理:进行性运动性失语症患者。

Clinical Reasoning: a woman with rapidly progressive apraxia.

机构信息

Department of Neurology, Northwestern University Feinberg School of Medicine, Chicago IL, USA.

出版信息

Neurology. 2013 Apr 9;80(15):e162-5. doi: 10.1212/WNL.0b013e31828c2eb8.

DOI:10.1212/WNL.0b013e31828c2eb8
PMID:23569002
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3662266/
Abstract

A 56-year-old woman presented with changes in balance, handwriting, and thinking. Approximately 1 year before her first visit, the patient developed difficulty walking, which caused multiple falls without serious injury. She also developed bilateral upper-extremity tremors that worsened with movement. At the time of her visit, she could barely sign her name.

摘要

一位 56 岁女性出现平衡、书写和思维改变。大约在首次就诊前 1 年,患者出现行走困难,导致多次摔倒但无严重损伤。她还出现双侧上肢震颤,活动时加重。就诊时,她几乎无法签名。