Keeling Lisa, Gordon Catherine, Sawaya David, Giles Henry, Nowicki Michael
Division of Pediatric Gastroenterology, University of Mississippi Medical Center, Jackson, MS, U.S.A.
Am J Case Rep. 2012;13:128-32. doi: 10.12659/AJCR.883234. Epub 2012 Jun 29.
Synovial sarcoma (SS) is an uncommon malignant neoplasm arising from primitive pluripotential mesenchyme primarily affecting the soft tissues of the extremities. Rarely other locations are involved, including the mediastinum.
After treatment for mediastinal SS by surgical resection, radiation therapy, and chemotherapy, an 11-year-old boy developed an esophageal stricture and fistula, the latter resulting in a paraesophageal abscess. Management of the esophageal stricture and fistula required a multi-disciplinary approach. We report our experience with the management of this difficult complication, as well as a brief review of the literature on SS.
Rare conditions, particularly those with unusual complications, present therapeutic challenges requiring a multi-disciplinary team approach. Reporting experiences with difficult cases can benefit providers faced with similar problems in the future.
滑膜肉瘤(SS)是一种罕见的恶性肿瘤,起源于原始多能间充质,主要累及四肢软组织。很少累及其他部位,包括纵隔。
一名11岁男孩在接受纵隔滑膜肉瘤手术切除、放射治疗和化疗后,出现食管狭窄和瘘管,后者导致食管旁脓肿。食管狭窄和瘘管的处理需要多学科方法。我们报告了我们处理这一困难并发症的经验,并对滑膜肉瘤的文献进行了简要综述。
罕见疾病,尤其是那些伴有不寻常并发症的疾病,带来了治疗挑战,需要多学科团队方法。报告疑难病例的经验可以使未来面临类似问题的医疗人员受益。