Kesieme Emeka B, Dongo Andrew E, Affusim Christopher, Prisadov Georgi, Okonta Kelechi, Imoloamen Clement
Department of Surgery, Irrua Specialist Teaching Hospital, PMB 8, Irrua, Edo State, Nigeria.
Case Rep Pulmonol. 2013;2013:619729. doi: 10.1155/2013/619729. Epub 2013 Mar 20.
Intrathoracic tumours in patients with Von Recklinghausen's disease have been widely reported, but there are very few cases of reported intrathoracic giant benign neurofibroma with marked mediastinal shift and superior vena cava syndrome. Patients that present with this pathology should be adequately investigated. Surgical resection has been considered curative.
冯·雷克林霍增氏病患者的胸内肿瘤已有广泛报道,但胸内巨大良性神经纤维瘤伴明显纵隔移位和上腔静脉综合征的报道却非常少见。出现这种病理情况的患者应进行充分检查。手术切除被认为可治愈。