Arthritis & Clinical Immunology Program, Oklahoma Medical Research Foundation, Oklahoma City, OK, USA.
Clin Exp Immunol. 2013 Jul;173(1):67-75. doi: 10.1111/cei.12094.
Sjögren's syndrome is a chronic illness manifested characteristically by immune injury to the salivary and lacrimal glands, resulting in dry mouth/eyes. Anti-Ro [Sjögren's syndrome antigen A (SSA)] and anti-La [Sjögren's syndrome antigen B (SSB)] autoantibodies are found frequently in Sjögren's subjects as well as in individuals who will go on to develop the disease. Immunization of BALB/c mice with Ro60 peptides results in epitope spreading with anti-Ro and anti-La along with lymphocyte infiltration of salivary glands similar to human Sjögren's. In addition, these animals have poor salivary function/low saliva volume. In this study, we examined whether Ro-peptide immunization produces a Sjögren's-like illness in other strains of mice. BALB/c, DBA-2, PL/J, SJL/J and C57BL/6 mice were immunized with Ro60 peptide-274. Sera from these mice were studied by immunoblot and enzyme-linked immunosorbent assay for autoantibodies. Timed salivary flow was determined after pharmacological stimulation, and salivary glands were examined pathologically. We found that SJL/J mice had no immune response to the peptide from Ro60, while C57BL/6 mice produced antibodies that bound the peptide but had no epitope spreading. PL/J mice had epitope spreading to other structures of Ro60 as well as to La, but like C57BL/6 and SJL/J had no salivary gland lymphocytic infiltration and no decrement of salivary function. DBA-2 and BALB/c mice had infiltration but only BALB/c had decreased salivary function. The immunological processes leading to a Sjögren's-like illness after Ro-peptide immunization were interrupted in a stepwise fashion in these differing mice strains. These data suggest that this is a model of preclinical disease with genetic control for epitope spreading, lymphocytic infiltration and glandular dysfunction.
干燥综合征是一种慢性疾病,其特征为免疫损伤唾液腺和泪腺,导致口干/眼干。抗 Ro [干燥综合征抗原 A(SSA)] 和抗 La [干燥综合征抗原 B(SSB)] 自身抗体在干燥综合征患者以及随后发生疾病的个体中经常发现。用 Ro60 肽免疫 BALB/c 小鼠会导致抗原表位扩展,出现抗 Ro 和抗 La,以及类似人类干燥综合征的唾液腺淋巴细胞浸润。此外,这些动物的唾液功能较差/唾液量低。在这项研究中,我们检查了 Ro-肽免疫是否会在其他品系的小鼠中产生类似干燥综合征的疾病。用 Ro60 肽-274 免疫 BALB/c、DBA-2、PL/J、SJL/J 和 C57BL/6 小鼠。通过免疫印迹和酶联免疫吸附试验研究这些小鼠的血清中的自身抗体。在药物刺激后测定定时唾液流量,并对唾液腺进行病理检查。我们发现 SJL/J 小鼠对 Ro60 肽没有免疫反应,而 C57BL/6 小鼠产生的抗体结合了该肽,但没有抗原表位扩展。PL/J 小鼠的抗原表位扩展到 Ro60 的其他结构以及 La,但与 C57BL/6 和 SJL/J 一样,没有唾液腺淋巴细胞浸润,也没有唾液功能减退。DBA-2 和 BALB/c 小鼠有浸润,但只有 BALB/c 小鼠的唾液功能下降。在这些不同的小鼠品系中,Ro-肽免疫后导致类似干燥综合征的疾病的免疫过程呈逐步中断。这些数据表明,这是一种具有遗传控制的抗原表位扩展、淋巴细胞浸润和腺体功能障碍的临床前疾病模型。