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与史蒂文斯-约翰逊综合征相关的快速进展性闭塞性细支气管炎

Rapidly progressive bronchiolitis obliterans associated with Stevens-Johnson syndrome.

作者信息

Tsunoda N, Iwanaga T, Saito T, Kitamura S, Saito K

机构信息

Department of Pulmonary Medicine, Jichi Medical School Hospital, Tochigi, Japan.

出版信息

Chest. 1990 Jul;98(1):243-5. doi: 10.1378/chest.98.1.243.

Abstract

A middle-aged woman developed fulminant respiratory failure during recovery from Stevens-Johnson syndrome. Mechanical ventilation was difficult because of unusually high airway pressures, and she died one month later. Autopsy revealed not only the usual features of bronchiolitis obliterans, but also obstruction of cartilaginous bronchi. The histopathologic features suggested a relationship between bronchial obstruction and Stevens-Johnson syndrome.

摘要

一名中年女性在史蒂文斯-约翰逊综合征恢复期出现暴发性呼吸衰竭。由于气道压力异常高,机械通气困难,一个月后死亡。尸检不仅发现了闭塞性细支气管炎的常见特征,还发现了软骨性支气管阻塞。组织病理学特征提示支气管阻塞与史蒂文斯-约翰逊综合征之间存在关联。

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