Jain Eety, Valiathan Ashima, Kumar Santosh, Natrajan Madhumitha
Department of Orthodontics and Dentofacial Orthopedics, Manipal College of Dental Sciences, Manipal, India.
Orthodontics (Chic.). 2013;14(1):e150-5. doi: 10.11607/ortho.947.
Osteogenesis imperfecta is a bone disorder in which three factors that influence bone strength (quality, mass, and geometry of osseous tissue) are affected. Pneumatization refers to the development of air-filled cavities inside the bone. Knowledge about these air-filled cavities provides valuable information for understanding the diagnosis and spread of various pathologic entities like hemangiomas, giant cell tumors, eosinophilic granulomas, and even metastatic tumor deposits. This paper presents a case in which radiologic, clinical, biochemical, and karyotypic evaluations lead to a diagnosis of osteogenesis imperfecta.
成骨不全是一种骨骼疾病，其中影响骨强度的三个因素（骨组织的质量、数量和几何形状）受到影响。骨气化是指骨内充满空气的腔隙的发育。关于这些充满空气的腔隙的知识为理解各种病理实体如血管瘤、巨细胞瘤、嗜酸性肉芽肿甚至转移性肿瘤沉积物的诊断和扩散提供了有价值的信息。本文介绍了一例通过放射学、临床、生化和核型评估诊断为成骨不全的病例。
