Department of Obstetrics and Gynecology, Beijing Anzhen Hospital of Capital Medical University, Beijing, China.
Am J Med Sci. 2013 Nov;346(5):385-9. doi: 10.1097/MAJ.0b013e31829338fb.
Eisenmenger's syndrome is characterized by a right-to-left or bidirectional shunt in congenital heart diseases. Hemolysis, elevated liver enzymes and low platelet count (HELLP) syndrome, commonly occurring during pregnancy, includes hemolysis, elevated liver enzymes and low platelet counts. HELLP syndrome and pregnancy are extremely rare in patients with Eisenmenger's syndrome. The authors report 4 cases of pregnancy complicated by the HELLP and Eisenmenger's syndrome and describe their initial intervention and the in-hospital outcomes of these cases. Special emphasis is given to elaborate about the hemodynamic monitoring, magnesium sulphate for convulsions, corticosteroid treatment, anticoagulation therapy, management of pulmonary hypertension, the timing of delivery, and blood product transfusion.
艾森曼格综合征的特征是先天性心脏病中的右向左或双向分流。溶血性贫血、肝酶升高和血小板计数降低（HELLP）综合征常见于妊娠期，包括溶血、肝酶升高和血小板计数降低。HELLP 综合征和妊娠在艾森曼格综合征患者中极为罕见。作者报告了 4 例妊娠合并 HELLP 和艾森曼格综合征的病例，并描述了他们的初步干预措施以及这些病例的住院结果。特别强调了详细阐述血流动力学监测、硫酸镁治疗惊厥、皮质类固醇治疗、抗凝治疗、肺动脉高压管理、分娩时机和血液制品输注。
