蛋白质错误折叠疾病：以α-1抗胰蛋白酶缺乏症为例 - Suppr

Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

作者信息

Silverman Gary A, Pak Stephen C, Perlmutter David H

机构信息

Department of Pediatrics, University of Pittsburgh School of Medicine, Children's Hospital of Pittsburgh and Magee Women's Hospital of University of Pittsburgh Medical Center, Pittsburgh, PA 15224, USA.

出版信息

J Pediatr. 2013 Aug;163(2):320-6. doi: 10.1016/j.jpeds.2013.03.077. Epub 2013 May 8.

DOI:10.1016/j.jpeds.2013.03.077

PMID:23664631

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3725216/

Abstract

摘要

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ad67/3725216/0798ff0cd2c9/nihms478429f1.jpg

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Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.蛋白质错误折叠疾病：以α-1抗胰蛋白酶缺乏症为例

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Disorders of protein misfolding: alpha-1-antitrypsin deficiency as prototype.

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