Montemurro Nicola, Perrini Paolo, Vannozzi Riccardo
Department of Neurosurgery, Azienda Ospedaliero Universitaria Pisana , Cisanello - Pisa , Italy.
Br J Neurosurg. 2013 Dec;27(6):838-9. doi: 10.3109/02688697.2013.798860. Epub 2013 May 22.
Langerhans cell histiocytosis, also known as histiocytosis X, is a rare proliferative disorder of histiocytes. Spinal involvement in the course of Langerhans cell histiocytosis in adult is rare, and epidural location is exceptional. We present a rare case of epidural involvement by Langerhans cell histiocytosis in a 71-year-old man to highlight the importance of considering Langerhans cell histiocytosis in the differential diagnosis of epidural spinal cord compression.
朗格汉斯细胞组织细胞增多症,也称为组织细胞增多症X,是一种罕见的组织细胞增殖性疾病。成人朗格汉斯细胞组织细胞增多症病程中累及脊柱的情况罕见,硬膜外受累则更为少见。我们报告一例71岁男性朗格汉斯细胞组织细胞增多症硬膜外受累的罕见病例,以强调在硬膜外脊髓压迫的鉴别诊断中考虑朗格汉斯细胞组织细胞增多症的重要性。