Hiradfar Mehran, Shojaeian Reza, Dehghanian Paria, Hajian Sara
Department of Pediatric Surgery, Mashhad University of Medical Sciences, Mashhad, Iran.
BMJ Case Rep. 2013 May 31;2013:bcr2012007524. doi: 10.1136/bcr-2012-007524.
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a multisystemic disorder in which impaired intestinal motor activity causes recurrent symptoms of intestinal obstruction in the absence of mechanical occlusion, associated with bladder distention without distal obstruction of the urinary tract. MMIHS and prune belly syndrome may overlap in most of the clinical features and discrimination of these two entities is important because the prognosis, management and consulting with parents are completely different. MMIHS outcome is very poor and in this article we present two neonates with MMIHS that both died in a few days.
巨膀胱-小结肠-肠蠕动不良综合征（MMIHS）是一种多系统疾病，其中肠道运动活动受损会在没有机械性梗阻的情况下导致反复出现肠梗阻症状，并伴有膀胱扩张而无尿路远端梗阻。MMIHS和梅干腹综合征在大多数临床特征上可能重叠，区分这两种疾病很重要，因为它们的预后、治疗以及与家长的沟通完全不同。MMIHS的预后非常差，在本文中，我们介绍了两名患有MMIHS的新生儿，他们均在数天内死亡。
