Verma Rajesh, Vasudevan Biju, Pragasam Vijendran, Dabbas Disha
Department of Dermatology, Command Hospital (Southern Command), Wanowrie, Pune, Maharashtra, India.
Indian Dermatol Online J. 2013 Apr;4(2):115-8. doi: 10.4103/2229-5178.110637.
A 19-year-old male presented with complaints of fluid-filled lesions on the body of 2 weeks duration. On examination, he was found to have multiple tense bullae distributed on the flexures, face, and genitalia with associated oral ulcers and "cluster of jewels" sign. The diagnosis was confirmed by histopathology and direct immunofluorescence. There are very few reports of linear IgA earlier from India according to the literature available so far, that too from the Southern part of the country. The patient had bullous pemphigoid-like lesions typically seen in adults, but the distribution of lesions was akin to that of the "chronic bullous disease of childhood variant" found in children. This case has been reported for rarity in this region and also because the patient had atypical morphology and distribution of lesions.
一名19岁男性因身上出现充满液体的皮损2周前来就诊。检查发现，他有多个紧张性大疱，分布于屈侧、面部和生殖器，伴有口腔溃疡及“宝石串”征。组织病理学和直接免疫荧光检查确诊了该诊断。根据目前可得的文献，印度此前关于线状IgA的报道极少，且均来自该国南部地区。该患者有成人中常见的类大疱性类天疱疮皮损，但皮损分布类似于儿童中发现的“儿童慢性大疱性疾病变异型”。报道此病例是因为该区域罕见，且患者皮损形态和分布不典型。
