Atili A, Richter C, Bahn E, Rustenbeck H H, Schittkowski M
Bereich Strabologie und Neuroophthalmologie, Augen-Praxis-Klink Esslingen, Adlerstr. 6, 73728, Esslingen, Deutschland,
Ophthalmologe. 2013 Nov;110(11):1051-7. doi: 10.1007/s00347-013-2815-0.
This paper summarizes the possible ocular manifestations of Churg-Straus syndrome (CCS) from the literature and presents an unusual case report from routine clinical practice with conjunctival granuloma, orbital pseudotumor and choroidal folds. The CSS is an ANCA-associated granulomatous vasculitis which can be manifested in various organs and represents a life-threatening situation for the patient. Ocular manifestations are rare and can spread to all segments of the eye and orbit. The most frequent forms of ocular involvement described in the literature are retinal occlusion and orbital pseudotumor with various degrees of expression.
本文从文献中总结了变应性肉芽肿性血管炎(CSS)可能出现的眼部表现,并呈现了1例来自日常临床实践的罕见病例报告,该病例有结膜肉芽肿、眼眶假瘤和脉络膜皱褶。CSS是一种抗中性粒细胞胞浆抗体相关的肉芽肿性血管炎,可累及多个器官,对患者生命构成威胁。眼部表现较为罕见,可累及眼和眼眶的各个部位。文献中描述的最常见的眼部受累形式是视网膜血管阻塞和不同程度表现的眼眶假瘤。