Dogra Shruti, Yadav Yogesh Kumar, Sharma Uma, Gupta Kusum
Department of Pathology, Safdarjung Hospital and Vardhman Mahavir Medical College, New Delhi, India.
Int J Trichology. 2012 Oct;4(4):278-9. doi: 10.4103/0974-7753.111203.
Rapunzel syndrome is a rare type of presentation of trichobezoar, an extension of hair fibers into the small bowel and rarely beyond the ileocecal valve. Its clinical presentation is deceptive ranging from abdominal mass to symptoms of obstruction. We report a 8-year-old girl admitted with a history of abdominal pain and vomiting off and on for a period of 1 year. Ultrasound findings were suggestive of subacute intestinal obstruction. On laparotomy, trichobezoar was found in the stomach extending into small bowel and was removed. Appendix was inflammed hence it was also resected. Microscopic evidence of a hair shaft was seen in the appendix indicating appendicitis was due to luminal obstruction by hair concretions.
长发公主综合征是毛粪石的一种罕见表现形式，即毛发纤维延伸至小肠，很少超过回盲瓣。其临床表现具有欺骗性，从腹部肿块到梗阻症状不等。我们报告一名8岁女孩，断断续续腹痛和呕吐1年。超声检查结果提示亚急性肠梗阻。剖腹手术时，发现胃内有毛粪石延伸至小肠并被切除。阑尾发炎，因此也被切除。阑尾中可见毛干的微观证据，表明阑尾炎是由毛发结石引起的管腔梗阻所致。
