Al Wadan Ali H, Al Kaff Hamed, Al Senabani Jamila, Al Saadi Azan S
Kwait University Hospital, Sana'a medical SchooL, Wadi Dhaher Road, P,O, Box 1247, Sana'a, Yemen.
Cases J. 2008 Oct 2;1(1):205. doi: 10.1186/1757-1626-1-205.
Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms.
We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia. In majority of the cases the diagnosis was made very late in the history of the disease, at a stage where surgery is the only cure for this syndrome.
In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.
长发公主综合征是一种罕见的毛粪石类型，毛发可延伸至小肠。临床表现具有欺骗性且模糊不清，从腹部肿块到胃肠道症状不等。
我们报告一名患有长发公主综合征的7岁女孩，起初完全未怀疑有毛粪石，尤其是在无吞食毛发病史的情况下。在大多数病例中，诊断在疾病过程中很晚才做出，此时手术是该综合征的唯一治疗方法。
在有长期胃肠道症状病史的儿童年龄组中，内镜检查是一种诊断和治疗方式，可能会减少毛粪石的手术治疗。
