Kumar Mritunjay, Maletha Madhukar, Bhuddi Sakshi, Kumari Rashmi
Department of Pediatrics and Neonatology, Apollomedics Super Speciality Hospital, Lucknow, Uttar Pradesh, India.
Department of Pediatric Surgery, SGRR Institute of Medical Sciences, Dehradun, Uttarakhand, India.
J Indian Assoc Pediatr Surg. 2020 Mar-Apr;25(2):112-114. doi: 10.4103/jiaps.JIAPS_1_19. Epub 2020 Jan 28.
Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague, ranging from asymptomatic abdominal mass to gastrointestinal perforation. There are only few cases reported in literature, with the youngest age being 3 years. We present the case of a 3-year-old male child presenting with Rapunzel syndrome and features of subacute intestinal obstruction.
长发公主综合征是一种罕见的毛粪石类型,毛发可延伸至小肠。临床表现具有欺骗性且模糊不清,从无症状的腹部肿块到胃肠道穿孔不等。文献中仅报道了少数病例,最小年龄为3岁。我们报告了一例3岁男童患长发公主综合征并伴有亚急性肠梗阻特征的病例。