Wabada S, Abubakar A S, Adamu A I, Kabir A, Gana L B
Paediatric Surgery Unit, Department of Surgery, University of Maiduguri Teaching Hospital, Maiduguri. Borno State, Nigeria.
Department of Anaesthesia and intensive Care, University of Maiduguri Teaching Hospital,Maiduguri. Borno State, Nigeria.
Niger J Clin Pract. 2017 Mar;20(3):388-391. doi: 10.4103/1119-3077.201427.
Wilms' tumour originates predominantly in the renal tissue; in rare cases it can also arise from extra-renal sites accounting for 0.5-1% of cases of Wilms' tumours seen. A diagnosis of extra-renal Wilms' cannot be easily established with clinical and radiological features except when the histological facts are provided. Wilms' tumours arising from extra-renal sites may not be different in clinical features, protocol of treatment and outcome from a typical intra renal Wilms' tumour. A 2-year-old boy presented with an asymptomatic abdominal swelling for 3 months. Abdominal ultrasound and CT scans revealed an extra-renal mass. Intravenous urogram (IVU) showed prompt excretion bilaterally. Post excision histology of the tumour confirmed a Wilms' tumour.
肾母细胞瘤主要起源于肾组织；在罕见情况下，它也可起源于肾外部位，占所见到的肾母细胞瘤病例的0.5 - 1%。除非提供组织学依据，仅依靠临床和放射学特征不容易确诊肾外肾母细胞瘤。起源于肾外部位的肾母细胞瘤在临床特征、治疗方案及预后方面可能与典型的肾内肾母细胞瘤并无差异。一名2岁男孩出现无症状腹部肿块3个月。腹部超声和CT扫描显示为肾外肿块。静脉肾盂造影（IVU）显示双侧排泄正常。肿瘤切除后的组织学检查证实为肾母细胞瘤。
