Reddy S C, Chopra P S, Rao P S
Department of Pediatrics, Saint Louis University School of Medicine, MO 63104, USA.
Am Heart J. 1997 Jan;133(1):112-9. doi: 10.1016/s0002-8703(97)70256-4.
Aneurysm of the membranous ventricular septum causing subpulmonic obstruction in patients with corrected transposition is rare but well documented. Higher left-sided (morphologic right) ventricular pressure causes protrusion of the aneurysm into the pulmonary outflow tract of the right-sided morphologic left ventricle, causing obstruction related to lack of conus and proximity of the aneurysm to subpulmonary region. Echo Doppler studies and angiography are useful in making a correct diagnosis. Surgical resection of the aneurysm along with closure of the ventricular septal defect is the treatment of choice. The prognosis is likely to be excellent.
矫正性大动脉转位患者中,膜周部室间隔瘤导致肺下梗阻罕见但有充分文献记载。较高的左侧(形态学右心室)心室压力导致瘤体突入右侧形态学左心室的肺流出道,因缺乏圆锥及瘤体靠近肺下区域而引起梗阻。超声多普勒检查和血管造影有助于做出正确诊断。手术切除瘤体并关闭室间隔缺损是首选治疗方法。预后可能极佳。