Costa Almeida C E, Reis Luis S, Almeida Carlos M Costa
Centro Hospitalar Universitário de Coimbra (Covões), Cirurgia C, Portugal.
Int J Surg Case Rep. 2013;4(9):778-81. doi: 10.1016/j.ijscr.2013.06.006. Epub 2013 Jun 20.
Bochdalek hernia is one of the most common congenital abnormalities manifested in infants. In the adult is a rarity, with a prevalence of 0.17-6% of all diaphragmatic hernias. Right-sided Bochdalek hernias containing colon are even more rare, with no case described in the literature with ileo-cecal appendix.
The authors present a case of a right-sided Bochdalek hernia in an adult female of 49 years old, presented with severe respiratory failure. During laparotomy for hernia correction, were found in an intrathoracic position the cecum and ileo-cecal appendix, the right colon and the transverse colon.
Although useful in patient evaluation, clinical history and physical examination are not helpful in making diagnosis because of their nonspecific character. CT scan is the most accurate exam for making diagnosis. Most of the times there is no hernial sac. Surgery is the treatment of choice, and it is always indicated even if asymptomatic. In general suture of the defect is possible. Due to patient's weak respiratory function we chose laparotomy by Kocher incision.
Being the first case of a right-sided Bochdalek hernia in the adult with a herniated ileo-cecal appendix, we name it Almeida-Reis hernia.
波奇代克疝是婴儿中最常见的先天性异常之一。在成人中较为罕见,占所有膈疝的0.17% - 6%。含结肠的右侧波奇代克疝更为罕见,文献中尚无伴有回盲部阑尾的病例描述。
作者报告一例49岁成年女性的右侧波奇代克疝病例,该患者出现严重呼吸衰竭。在进行疝修补的剖腹手术中,发现盲肠、回盲部阑尾、右结肠和横结肠位于胸腔内。
尽管临床病史和体格检查对患者评估有用,但因其缺乏特异性,对诊断并无帮助。CT扫描是最准确的诊断检查。大多数情况下没有疝囊。手术是首选治疗方法,即使无症状也应进行手术。一般来说,缺损缝合是可行的。由于患者呼吸功能较弱,我们选择经科赫尔切口进行剖腹手术。
作为首例成年右侧波奇代克疝伴回盲部阑尾疝出的病例,我们将其命名为阿尔梅达 - 雷斯疝。