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脊髓性肌阵挛:它总是心因性的吗?

Propriospinal myoclonus: is it always psychogenic?

作者信息

Verma Rajesh, Praharaj Heramba Narayan, Raut Tushar Premraj, Rai Dheeraj

机构信息

Department of Neurology, King George Medical University, Lucknow, Uttar Pradesh, India.

出版信息

BMJ Case Rep. 2013 Jul 29;2013:bcr2013009559. doi: 10.1136/bcr-2013-009559.

DOI:10.1136/bcr-2013-009559
PMID:23901073
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3736211/
Abstract

Propriospinal myoclonus (PSM) is a rare type of movement disorder in which the myoclonic jerks are present or intensified in supine position. Arising from a thoracic or abdominal generator, the movements propagate rostrocaudally as per the spinospinal conduction velocity. Routine neuroimaging and electrophysiology being normal in most instances, it is frequently interpreted as psychogenic. We present a case of PSM which will throw ample light on the pathophysiology, approach and dilemmas in treatment.

摘要

脊髓性肌阵挛(PSM)是一种罕见的运动障碍类型,其肌阵挛性抽搐在仰卧位时出现或加重。该运动源于胸段或腹段的起博点,按照脊髓传导速度向头尾方向传播。在大多数情况下,常规神经影像学和电生理学检查结果正常,因此常被认为是心因性的。我们报告一例脊髓性肌阵挛病例,该病例将为其病理生理学、治疗方法及困境提供充分的见解。

相似文献

1
Propriospinal myoclonus: is it always psychogenic?脊髓性肌阵挛:它总是心因性的吗?
BMJ Case Rep. 2013 Jul 29;2013:bcr2013009559. doi: 10.1136/bcr-2013-009559.
2
Clinical diagnosis of propriospinal myoclonus is unreliable: an electrophysiologic study.临床诊断 propriospinal 肌阵挛不可靠:一项电生理研究。
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Axial jerks: a clinical spectrum ranging from propriospinal to psychogenic myoclonus.轴向痉挛:一种从本体感受性痉挛到心因性肌阵挛的临床谱。
J Neurol. 2010 Aug;257(8):1349-55. doi: 10.1007/s00415-010-5531-6. Epub 2010 Mar 30.
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Propriospinal myoclonus: utility of magnetic resonance diffusion tensor imaging and fiber tracking.脊髓性肌阵挛:磁共振扩散张量成像和纤维束示踪的应用价值
Mov Disord. 2007 Jul 30;22(10):1506-1509. doi: 10.1002/mds.21562.
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Propriospinal myoclonus revisited: Clinical, neurophysiologic, and neuroradiologic findings.再探脊髓性肌阵挛:临床、神经生理学及神经放射学表现
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Propriospinal myoclonus at sleep onset.睡眠起始时的脊髓性肌阵挛
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Propriospinal myoclonus: The spectrum of clinical and neurophysiological phenotypes.脊髓_proprio 反射性肌阵挛:临床和神经生理学表型谱。
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Axial myoclonus of propriospinal origin.脊髓固有性起源的轴索性肌阵挛
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Psychogenic propriospinal myoclonus.心理性脊髓固有肌阵挛
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本文引用的文献

1
Reversible propriospinal myoclonus due to thoracic disc herniation: long-term follow-up.因胸椎间盘突出导致的可逆转的 propriospinal 肌阵挛:长期随访。
J Neurol Sci. 2012 Feb 15;313(1-2):32-4. doi: 10.1016/j.jns.2011.09.036. Epub 2011 Oct 20.
2
Management of patients with myoclonus: available therapies and the need for an evidence-based approach.肌阵挛患者的治疗管理:现有疗法及对循证方法的需求。
Lancet Neurol. 2010 Oct;9(10):1028-36. doi: 10.1016/S1474-4422(10)70193-9.
3
Axial jerks: a clinical spectrum ranging from propriospinal to psychogenic myoclonus.轴向痉挛:一种从本体感受性痉挛到心因性肌阵挛的临床谱。
J Neurol. 2010 Aug;257(8):1349-55. doi: 10.1007/s00415-010-5531-6. Epub 2010 Mar 30.
4
Propriospinal myoclonus following intrathecal bupivacaine in hip surgery: a case report.椎管内布比卡因用于髋关节手术后引发的 propriospinal 肌阵挛:病例报告。
Minerva Anestesiol. 2010 Apr;76(4):290-3. Epub 2009 Dec 23.
5
Propriospinal myoclonus revisited: Clinical, neurophysiologic, and neuroradiologic findings.再探脊髓性肌阵挛:临床、神经生理学及神经放射学表现
Neurology. 2009 Apr 14;72(15):1301-9. doi: 10.1212/WNL.0b013e3181a0fd50.