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脊髓性肌阵挛:它总是心因性的吗?

Propriospinal myoclonus: is it always psychogenic?

作者信息

Verma Rajesh, Praharaj Heramba Narayan, Raut Tushar Premraj, Rai Dheeraj

机构信息

Department of Neurology, King George Medical University, Lucknow, Uttar Pradesh, India.

出版信息

BMJ Case Rep. 2013 Jul 29;2013:bcr2013009559. doi: 10.1136/bcr-2013-009559.

Abstract

Propriospinal myoclonus (PSM) is a rare type of movement disorder in which the myoclonic jerks are present or intensified in supine position. Arising from a thoracic or abdominal generator, the movements propagate rostrocaudally as per the spinospinal conduction velocity. Routine neuroimaging and electrophysiology being normal in most instances, it is frequently interpreted as psychogenic. We present a case of PSM which will throw ample light on the pathophysiology, approach and dilemmas in treatment.

摘要

脊髓性肌阵挛(PSM)是一种罕见的运动障碍类型,其肌阵挛性抽搐在仰卧位时出现或加重。该运动源于胸段或腹段的起博点,按照脊髓传导速度向头尾方向传播。在大多数情况下,常规神经影像学和电生理学检查结果正常,因此常被认为是心因性的。我们报告一例脊髓性肌阵挛病例,该病例将为其病理生理学、治疗方法及困境提供充分的见解。

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