• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利：CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法，用中文像聊天一样搜索，搜遍4000万医学文献。AI智能推荐，让科研检索更轻松。

立即免费搜索

文件翻译

保留排版，准确专业，支持PDF/Word/PPT等文件格式，支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述，25分钟生成高质量综述，智能提取关键信息，辅助科研写作。

立即免费体验

罕见中的罕见：肺恶性血管周上皮样细胞瘤。

Uncommon of the uncommon: malignant perivascular epithelioid cell tumor of the lung.

机构信息

Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul 135-710, Korea.

出版信息

Korean J Radiol. 2013 Jul-Aug;14(4):692-6. doi: 10.3348/kjr.2013.14.4.692. Epub 2013 Jul 17.

DOI:10.3348/kjr.2013.14.4.692
PMID:23901329
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3725366/
Abstract

A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.

摘要

血管周上皮样细胞瘤是一种罕见的间叶性肿瘤，其特征为大量细胞质过碘酸希夫阳性糖原（也因其特征而被称为糖瘤或肺透明细胞肿瘤），且多为良性。我们报告了 1 例 63 岁男性，其胸部 X 线片显示肿块增大。经过全面检查，诊断为恶性肺血管周上皮样细胞瘤伴肺内转移。本文描述了我们所面临的诊断和治疗困难。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1219/3725366/dd141a0bff8e/kjr-14-692-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1219/3725366/dd141a0bff8e/kjr-14-692-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/1219/3725366/dd141a0bff8e/kjr-14-692-g001.jpg

相似文献

1
Uncommon of the uncommon: malignant perivascular epithelioid cell tumor of the lung.罕见中的罕见：肺恶性血管周上皮样细胞瘤。
Korean J Radiol. 2013 Jul-Aug;14(4):692-6. doi: 10.3348/kjr.2013.14.4.692. Epub 2013 Jul 17.
2
PEComa (clear cell "sugar" tumor) of the lung: a benign tumor that presented with thrombocytosis.肺透明细胞“糖”瘤（PEComa）：一种表现为血小板增多症的良性肿瘤。
Ann Thorac Surg. 2009 Dec;88(6):2013-5. doi: 10.1016/j.athoracsur.2009.05.041.
3
Clear cell "sugar" tumor of the lung: benign or malignant?肺透明细胞“糖”瘤：良性还是恶性？
Int Surg. 2015 May;100(5):924-6. doi: 10.9738/INTSURG-D-14-00021.1.
4
Malignant perivascular epithelioid cell neoplasm of the mediastinum and the lung: one case report.纵隔及肺恶性血管周上皮样细胞瘤1例报告
Medicine (Baltimore). 2015 Jun;94(22):e904. doi: 10.1097/MD.0000000000000904.
5
Clear cell "sugar" tumor of the lung: Diagnostic characteristics of a rare pulmonary tumor: A case report and review of literature.肺透明细胞“糖”瘤：一种罕见肺肿瘤的诊断特征：病例报告及文献复习。
Medicine (Baltimore). 2023 Feb 17;102(7):e33035. doi: 10.1097/MD.0000000000033035.
6
Clear cell sugar tumor of the lung masquerading as tuberculosis in a pediatric patient.一名儿科患者中伪装成肺结核的肺透明细胞糖瘤。
J Thorac Cardiovasc Surg. 2010 May;139(5):e108-9. doi: 10.1016/j.jtcvs.2009.03.037. Epub 2009 May 31.
7
[Pulmonary malignant perivascular epithelioid cell tumor mixed with lung adenocarcinoma components: a case report and literature review].[肺恶性血管周上皮样细胞瘤合并肺腺癌成分：1例报告及文献复习]
Zhonghua Jie He He Hu Xi Za Zhi. 2021 May 12;44(5):468-473. doi: 10.3760/cma.j.cn112147-20201119-01104.
8
Malignant perivascular epithelioid cell tumor of the kidney with rare pulmonary and ileum metastases.肾恶性血管周上皮样细胞瘤伴罕见肺和回肠转移
Int J Clin Exp Pathol. 2014 Aug 15;7(9):6357-63. eCollection 2014.
9
PEComa of the lung.肺血管周上皮样细胞瘤
J Cancer Res Ther. 2010 Jan-Mar;6(1):109-11. doi: 10.4103/0973-1482.63548.
10
Malignant perivascular epithelioid cell tumor of the lung synchronous with a primary adenocarcinoma: one case report and review of the literature.肺恶性血管周上皮样细胞肿瘤合并原发性腺癌：一例报告并文献复习。
BMC Cancer. 2019 Mar 15;19(1):235. doi: 10.1186/s12885-019-5383-0.

引用本文的文献

1
Malignant lung PEComa (clear cell tumor): rare case report and literature review.恶性肺PEComa（透明细胞瘤）：罕见病例报告及文献综述
Front Oncol. 2023 Sep 20;13:1260844. doi: 10.3389/fonc.2023.1260844. eCollection 2023.
2
Primary Perivascular Epithelioid Cell Tumor of the Lung: A Case Report.肺原发性血管周上皮样细胞瘤：一例报告
J Chest Surg. 2023 Sep 5;56(5):367-370. doi: 10.5090/jcs.22.139. Epub 2023 Mar 15.
3
Malignant perivascular epitheloid cell tumour (PEComa) of the lung - a rare entity.肺恶性血管周上皮样细胞瘤（PEComa）——一种罕见的疾病。

本文引用的文献

1
Clear cell 'sugar' tumour of the lung with malignant histological features and melanin pigmentation--the first reported case.具有恶性组织学特征及黑色素沉着的肺透明细胞“糖”瘤——首例报道病例
Histopathology. 2011 Feb;58(3):498-500. doi: 10.1111/j.1365-2559.2011.03773.x. Epub 2011 Feb 16.
2
Malignant PEComa: a case report with emphasis on clinical and morphological criteria.恶性PEComa：一例报告，重点关注临床和形态学标准。
BMC Surg. 2011 Jan 27;11:3. doi: 10.1186/1471-2482-11-3.
3
Malignant clear cell sugar tumor of the lung: patient case report.
Innov Surg Sci. 2017 Feb 23;2(1):39-42. doi: 10.1515/iss-2016-0032. eCollection 2017 Mar.
4
Malignant perivascular epithelioid cell tumor of the lung synchronous with a primary adenocarcinoma: one case report and review of the literature.肺恶性血管周上皮样细胞肿瘤合并原发性腺癌：一例报告并文献复习。
BMC Cancer. 2019 Mar 15;19(1):235. doi: 10.1186/s12885-019-5383-0.
5
PEComa of the Uterus: A Rare Mesenchymal Tumor Displaying a ≪Snowstorm≫ Pattern at Magnetic Resonance Imaging.子宫PEComa：一种罕见的间叶性肿瘤，在磁共振成像上表现为“暴风雪”样表现
J Belg Soc Radiol. 2016 Jan 29;100(1):5. doi: 10.5334/jbr-btr.926.
6
Computerized Tomography and Magnetic Resonance Imaging Findings in Malignant Perivascular Epithelioid Cell Tumors of the Ovaries with Pulmonary Metastasis.卵巢恶性血管周上皮样细胞瘤伴肺转移的计算机断层扫描和磁共振成像表现
Iran J Radiol. 2016 Aug 1;13(4):e34712. doi: 10.5812/iranjradiol.34712. eCollection 2016 Oct.
7
Clear cell tumor of the lung: Two case reports and a review of the literature.肺透明细胞瘤：两例病例报告及文献综述
Medicine (Baltimore). 2016 Aug;95(33):e4492. doi: 10.1097/MD.0000000000004492.
8
Primary retroperitoneal perivascular epithelioid cell neoplasm: A case report.原发性腹膜后血管周上皮样细胞肿瘤：一例报告。
Oncol Lett. 2015 Jul;10(1):469-472. doi: 10.3892/ol.2015.3210. Epub 2015 May 14.
9
Malignant perivascular epithelioid cell neoplasm of the mediastinum and the lung: one case report.纵隔及肺恶性血管周上皮样细胞瘤1例报告
Medicine (Baltimore). 2015 Jun;94(22):e904. doi: 10.1097/MD.0000000000000904.
肺恶性透明细胞糖瘤：病例报告
J Clin Oncol. 2010 Nov 1;28(31):e626-8. doi: 10.1200/JCO.2010.29.6939. Epub 2010 Aug 30.
4
Clinical activity of mTOR inhibition with sirolimus in malignant perivascular epithelioid cell tumors: targeting the pathogenic activation of mTORC1 in tumors.西罗莫司抑制 mTOR 在恶性血管周上皮样细胞肿瘤中的临床活性：针对肿瘤中 mTORC1 的致病激活。
J Clin Oncol. 2010 Feb 10;28(5):835-40. doi: 10.1200/JCO.2009.25.2981. Epub 2010 Jan 4.
5
Perivascular epithelioid cell tumor.血管周上皮样细胞肿瘤
Arch Pathol Lab Med. 2009 Apr;133(4):648-54. doi: 10.5858/133.4.648.
6
Clear cell "sugar" tumor of the lung: a well-enhanced mass with an early washout pattern on dynamic contrast-enhanced computed tomography.肺透明细胞“糖”瘤：动态对比增强计算机断层扫描上具有早期洗脱模式的强化良好的肿块。
J Korean Med Sci. 2008 Dec;23(6):1121-4. doi: 10.3346/jkms.2008.23.6.1121. Epub 2008 Dec 23.
7
PEComas: the past, the present and the future.血管周上皮样细胞瘤：过去、现在与未来
Virchows Arch. 2008 Feb;452(2):119-32. doi: 10.1007/s00428-007-0509-1. Epub 2007 Dec 14.
8
Pecoma of the lung: a benign tumor with extensive 18F-2-deoxy-D-glucose uptake.
Interact Cardiovasc Thorac Surg. 2007 Oct;6(5):676-8. doi: 10.1510/icvts.2007.154039. Epub 2007 Jun 7.
9
Metastatic PEComa to the brain.
Acta Neuropathol. 2006 Sep;112(3):349-51. doi: 10.1007/s00401-006-0105-5. Epub 2006 Jul 15.
10
Perivascular epithelioid cell neoplasms of soft tissue and gynecologic origin: a clinicopathologic study of 26 cases and review of the literature.软组织和妇科来源的血管周上皮样细胞肿瘤：26例临床病理研究及文献复习
Am J Surg Pathol. 2005 Dec;29(12):1558-75. doi: 10.1097/01.pas.0000173232.22117.37.