Na Hye Rim, Suh Jong Hui, Lee Jiyun
Department of Thoracic and Cardiovascular Surgery, Seoul St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea.
Department of Thoracic and Cardiovascular Surgery, Incheon St. Mary's Hospital, College of Medicine, The Catholic University of Korea, Incheon, Korea.
J Chest Surg. 2023 Sep 5;56(5):367-370. doi: 10.5090/jcs.22.139. Epub 2023 Mar 15.
Perivascular epithelioid cell tumors (PEComas) are very rare mesenchymal neoplasms, composed of histologically and immunohistochemically distinctive cells that form a sheet-like appearance around vessel lumens. Although most are benign, a malignant subset does exist, complicating clinical diagnostic efforts. Proper evaluation and management are thus essential for long-term patient survival. Herein, we present a rare case of a benign pulmonary PEComa that was diagnosed postoperatively in a 45-year-old woman.
血管周上皮样细胞瘤（PEComas）是非常罕见的间叶性肿瘤，由组织学和免疫组化上独特的细胞组成，这些细胞在血管腔周围形成片状外观。虽然大多数是良性的，但确实存在恶性亚型，这使临床诊断工作变得复杂。因此，正确的评估和管理对于患者的长期生存至关重要。在此，我们报告一例罕见的良性肺PEComa病例，该病例是在一名45岁女性患者术后确诊的。
