Suzuki Shoji, Kise Hiroaki, Kaga Shigeaki, Hoshiai Minako, Koizumi Keiichi, Hasebe Yohei, Motohashi Shinya, Matsumoto Masahiko
Department of Surgery, University of Yamanashi, 1110 Shimokato, Chuo-City, Yamanashi, 409-3898, Japan,
Gen Thorac Cardiovasc Surg. 2015 Aug;63(8):472-5. doi: 10.1007/s11748-013-0304-7. Epub 2013 Aug 3.
A boy, prenatally diagnosed as hypoplastic left heart syndrome (HLHS) with intact atrial septum (IAS) was successfully treated by hybrid procedures. He underwent emergent catheter atrial septostomy and stent insertion in the atrial septum on Day 1 and then underwent bilateral pulmonary artery banding, ductal stent insertion, modified Norwood operation, bidirectional Glenn's operation and finally Fontan type operation at 2 years of age. Considering the presence of decompression pathway from the left atrium in HLHS with IAS, we should organize a treatment team for collaborative work and plan an appropriate treatment strategy before delivery. Although his clinical course has been uneventful until now, closer medical observation is warranted because he may have coexisting pulmonary disease.
一名产前诊断为房间隔完整的左心发育不全综合征（HLHS）的男孩通过杂交手术成功治愈。他在出生第1天接受了紧急导管房间隔造口术及房间隔支架置入，随后接受了双侧肺动脉环缩术、动脉导管支架置入、改良诺伍德手术、双向格林手术，最终在2岁时接受了Fontan类手术。鉴于存在房间隔完整的HLHS患者左心房减压途径，我们应组建治疗团队进行协作，并在分娩前制定合适的治疗策略。尽管他目前临床过程平稳，但因其可能并存肺部疾病，仍需密切医学观察。
