Tavakolizadeh Sepideh, Farahi Azadeh
Noor Ophthalmology Research Center, Noor Eye Hospital, Tehran, Iran.
Korean J Ophthalmol. 2013 Aug;27(4):308-10. doi: 10.3341/kjo.2013.27.4.308. Epub 2013 Jul 23.
It is commonly accepted that albino patients with strabismus rarely achieve binocularity and depth perception after strabismus surgery. The presence of retino-geniculo-cortical misrouting, a hallmark of the visual system in albinism, does not necessarily cause total loss of binocular vision, however, not even in albino patients with strabismus. Recently some degrees of stereopsis were reported in albinism patients with minimal clinical nystagmus, if any, in the absence of strabismus. It is possible that patients with albinism and strabismus have binocular visual potential which appears after strabismus correction and provides appropriate postoperative alignment in the long term. Here we present two cases of clinically diagnosed oculocutaneous albinism, an 18-year-old girl and a 16-year-old boy, both with exotropia ≥40 prism diopter, who gained acceptable alignment and fusion after surgical correction of their strabismus as demonstrated on Bagolini testing. In cases of albinism accompanied by visual pathway abnormalities and strabismus, binocular visual potential is not impossible, and some levels can be expected. Thus, these patients, like other cases of strabismus, may benefit from treatment of strabismus at an earlier age to achieve appropriate alignment, cosmetic satisfaction, and a possibly increased chance of fusion.
人们普遍认为，白化病斜视患者斜视手术后很少能获得双眼视和深度感知。然而，视网膜 - 膝状体 - 皮质通路错接作为白化病视觉系统的一个标志，并不一定会导致双眼视力完全丧失，即使是患有斜视的白化病患者也不一定如此。最近有报道称，在没有斜视且临床眼球震颤极轻微（若有）的白化病患者中存在一定程度的立体视。白化病斜视患者有可能具有双眼视觉潜能，这种潜能在斜视矫正后会显现出来，并能在长期提供适当的术后眼位矫正。在此，我们报告两例临床诊断为眼皮肤白化病的病例，一名18岁女孩和一名16岁男孩，两人均为外斜视≥40棱镜度，经斜视手术矫正后，如巴戈利尼试验所示，获得了可接受的眼位矫正和融合。在伴有视觉通路异常和斜视的白化病病例中，双眼视觉潜能并非不可能存在，并且可以预期达到一定水平。因此，这些患者与其他斜视病例一样，可能受益于早期斜视治疗，以实现适当的眼位矫正、美容满意度，并可能增加融合的机会。
