Milani Gregorio Paolo, Dellepiane Rosa Maria, Castellazzi Massimo Luca, Mazzoni Marta Benedetta Maria, Bianchetti Mario Giovanni, Fossali Emilio Filippo
Pediatric Emergency Unit, Clinica De Marchi, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.
Pediatr Int. 2013 Aug;55(4):e81-2. doi: 10.1111/ped.12068.
Episodic idiopathic systemic capillary leak syndrome is a rare disorder that presents with attacks of circulatory shock due to plasma leakage into the extravascular space. Reported here is the case of a girl who had recurrent circulatory shock. The diagnosis of episodic idiopathic systemic capillary leak syndrome was made following the fourth episode. The course was favorable following acute i.v. cristalloids and methylprednisolone.
发作性特发性全身性毛细血管渗漏综合征是一种罕见疾病，因血浆渗漏至血管外间隙而引发循环性休克发作。本文报告了一名反复出现循环性休克的女孩病例。在第四次发作后确诊为发作性特发性全身性毛细血管渗漏综合征。经静脉输注晶体液和甲基强的松龙进行急性治疗后，病情好转。
