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特发性急性横贯性脊髓炎:静脉注射免疫球蛋白后完全康复。

Idiopathic acute transverse myelitis: Complete recovery after intravenous immunoglobulin.

作者信息

Pavlou E, Gkampeta A, Kouskouras K, Evangeliou A, Athanasiadou-Piperopoulou F

机构信息

2 Department of Pediatrics, Aristotle University of Thessaloniki, "AHEPA'' Hospital.

出版信息

Hippokratia. 2012 Jul;16(3):283-5.

Abstract

Idiopathic acute transverse myelitis is a focal inflammatory disorder of the spinal cord of unknown etiology diagnosed according to established criteria. As it occurs rarely in children herein we report a case of a 4 year old boy who developed clinical and radiological manifestations of myelitis, 10 days after a recent respiratory tract infection. Diagnostic workup failed to reveal a causative factor. After the administration of corticosteroids a clinical deterioration was observed and intravenous immunoglobulin was administered. Symptoms resolved within a 48-hour period, suggesting an immune-mediated pathogenetic mechanism.

摘要

特发性急性横贯性脊髓炎是一种病因不明的脊髓局灶性炎症性疾病,根据既定标准进行诊断。由于其在儿童中很少见,我们在此报告一例4岁男孩,在近期呼吸道感染10天后出现脊髓炎的临床和影像学表现。诊断性检查未能发现病因。给予皮质类固醇后观察到临床病情恶化,随后给予静脉注射免疫球蛋白。症状在48小时内缓解,提示免疫介导的发病机制。

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本文引用的文献

1
Laboratory diagnosis of Mycoplasma pneumoniae respiratory tract infections in children.儿童肺炎支原体呼吸道感染的实验室诊断
Eur J Clin Microbiol Infect Dis. 2007 Jul;26(7):513-5. doi: 10.1007/s10096-007-0326-0. Epub 2007 Jun 7.
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Mycoplasma pneumoniae-associated myelitis: a comprehensive review.肺炎支原体相关脊髓炎:全面综述
Eur J Neurol. 2006 Feb;13(2):112-24. doi: 10.1111/j.1468-1331.2006.01174.x.

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