di Libero Lorenzo, Varricchio Antonio, Tartaglia Ernesto, Iazzetta Igino, Tartaglia Alberto, Bernardo Antonella, Bernardo Rosanna, Triscino Giovangiuseppe, Conte Domenico Lo
Unità Funzionale di Chirurgia Generale e Specialistica, Clinica Sanatrix, Via San Domenico 31, Napoli, Direttore, Dott Alberto Tartaglia, Italy.
Int J Surg Case Rep. 2013;4(10):882-5. doi: 10.1016/j.ijscr.2013.06.021. Epub 2013 Jul 26.
Median arcuate ligament (MAL) malposition is a rare cause of celiac axis compression syndrome (CACS) or Dunbar syndrome.
A 26-year-old female presented with severe postprandial epigastric pain, weight loss, heartburn and regurgitation unresponsive to medical therapy. CT angiography and duplex ultrasound demonstrated the MAL crossing anterior to the celiac artery (CA). Reconstructions demonstrated CA compression, while the superior mesenteric artery (SMA) was normal. The MAL was laparoscopically divided, releasing the celiac axis. A concomitant Nissen fundoplication was performed. At 3-months follow-up, the CT-scan demonstrated no evidence of CACS with complete symptom resolution.
Dunbar's syndrome can be treated with endovascular surgery, laparoscopic MAL division or vascular surgery.Six anatomical and morphologic variations of aortic and esophageal hiatus are described. The result of the analysis of these anatomical data leads to the conclusion that hiatus hernia, Dunbar's syndrome and GERD have a common etiopathogenesis and physiopathology.
Laparoscopic treatment is useful and feasible in centers with experience in majorlaparoscopic surgery with reduced invasiveness, better cosmetic effect and shorter postoperative course.
正中弓状韧带(MAL)位置异常是腹腔干压迫综合征(CACS)或邓巴综合征的罕见病因。
一名26岁女性出现严重的餐后上腹部疼痛、体重减轻、烧心和反流,药物治疗无效。CT血管造影和双功超声显示MAL在腹腔干(CA)前方交叉。重建显示CA受压,而肠系膜上动脉(SMA)正常。通过腹腔镜将MAL分离,解除腹腔干压迫。同时进行了Nissen胃底折叠术。在3个月的随访中,CT扫描显示无CACS迹象,症状完全缓解。
邓巴综合征可通过血管内手术、腹腔镜MAL分离术或血管手术进行治疗。描述了主动脉裂孔和食管裂孔的六种解剖和形态变异。对这些解剖数据的分析结果得出结论,食管裂孔疝、邓巴综合征和胃食管反流病具有共同的病因和病理生理机制。
在有大型腹腔镜手术经验的中心,腹腔镜治疗是有用且可行的,具有侵袭性小、美容效果好和术后病程短的优点。