Cho Hyun Suk, Woo Ji Young, Hong Hye-Suk, Kim Yoo Na, Yang Ik, Lee Yul, Kim Han Myun
From the Department of Radiology, Hallym University College of Medicine, Kangnam Sacred Heart Hospital, Seoul, Republic of Korea.
J Comput Assist Tomogr. 2013 Sep-Oct;37(5):797-804. doi: 10.1097/RCT.0b013e31829ce256.
The objective of this study was to assess the imaging characteristics and classify congenital short pancreas on the basis of morphologic features on multidetector computed tomography (MDCT) and to determine the associated diseases and congenital anomalies of each type.
We conducted a retrospective search from 2006 to 2012 using the keywords "short pancreas," "agenesis or hypoplasia of the dorsal pancreas," or "hypoplasia of the ventral pancreas." Clinical data and images were analyzed; finally, 24 patients with congenital short pancreas were included in this study. Imaging features of the 3 types of congenital short pancreas and their associated anomalies on MDCT were evaluated.
Congenital short pancreas was classified into type 1 (agenesis or hypoplasia of the dorsal pancreas): no congenital anomaly but presence of diabetes mellitus (45%); type 2 (agenesis or hypoplasia of the pancreatic uncinate process): intestinal malrotation (100%); and type 3 (combined hypoplasia or agenesis of the uncinate process and dorsal pancreas): a spectrum of various congenital anomalies, including abdominal heterotaxy and abnormal spleen (100%).
Recognizing the spectrum of agenesis or hypoplasia of the pancreas and morphologic classification of congenital short pancreas on MDCT may help radiologists detect and understand disease associated with congenital short pancreas.
本研究的目的是评估先天性短胰腺的影像学特征，根据多排螺旋计算机断层扫描（MDCT）的形态学特征对其进行分类，并确定每种类型的相关疾病和先天性异常。
我们在2006年至2012年期间进行了一项回顾性检索，使用关键词“短胰腺”“背侧胰腺发育不全或发育不良”或“腹侧胰腺发育不良”。分析临床数据和图像；最终，本研究纳入了24例先天性短胰腺患者。评估了3种类型先天性短胰腺的影像学特征及其在MDCT上的相关异常。
先天性短胰腺分为1型（背侧胰腺发育不全或发育不良）：无先天性异常，但存在糖尿病（45%）；2型（胰腺钩突发育不全或发育不良）：肠旋转不良（100%）；3型（钩突和背侧胰腺联合发育不全或发育不良）：一系列各种先天性异常，包括内脏异位和脾脏异常（100%）。
认识胰腺发育不全或发育不良的范围以及MDCT上先天性短胰腺的形态学分类，可能有助于放射科医生检测和理解与先天性短胰腺相关的疾病。
