Sonkar Satyendra Kumar, Kumar Satish, Singh Neeraj Kumar
Department of Medicine, Chhatrapati Shahuji Maharaj Medical University (King George Medical University), Lucknow, India.
BMJ Case Rep. 2018 Feb 14;2018:bcr-2017-223301. doi: 10.1136/bcr-2017-223301.
Dorsal pancreatic agenesis is an extremely rare entity characterised by absence of body and tail of pancreas, while there are so many other developmental anomalies of the pancreas that have been reported. Here we report a 25-year-old young man who presented with pain in the abdomen, recurrent loose stools and hyperglycaemia. On radiological imaging study, there was complete agenesis of the dorsal pancreas except for thin stripe of tissue at the level of the uncinate process. Both exocrinedysfunction and endocrine dysfunction were present in this patient. Patient was supplemented with pancreatic enzyme preparation and insulin.
背侧胰腺发育不全是一种极其罕见的病症，其特征为胰腺体部和尾部缺失，而此前已有许多其他胰腺发育异常的报道。在此，我们报告一名25岁的年轻男性，他出现腹痛、反复腹泻和高血糖症状。经影像学检查，除钩突水平有一条薄组织条带外，背侧胰腺完全缺如。该患者同时存在外分泌功能障碍和内分泌功能障碍。患者接受了胰酶制剂和胰岛素补充治疗。
