Dunn E J, Ulicny K S, Wright C B, Gottesman L
Jewish Hospital of Cincinnati, Ohio.
Chest. 1990 Feb;97(2):338-46. doi: 10.1378/chest.97.2.338.
Sclerosing mediastinitis is an uncommon disease associated with a multiplicity of clinical syndromes. The cause of this disorder is probably an abnormal fibroproliferative response to an inflammatory stimulus, most commonly a granulomatous infection secondary to Histoplasma capsulatum. The pathophysiology of this disease is predicated on the encasement of mediastinal vital organ structures within a dense fibrotic mass. This mass appears to emanate from an invasive chronic inflammatory process causing erosion as well as external compression of these structures. The following case reports illustrate the diversity of this disease entity, representing a patient population from the Ohio River Valley, endemic for histoplasmosis. The purpose of this report is to elucidate the various clinical manifestations of sclerosing mediastinitis and to correlate the pathologic process with a rational approach to treatment.
硬化性纵隔炎是一种罕见疾病,与多种临床综合征相关。这种疾病的病因可能是对炎症刺激的异常纤维增生反应,最常见的是继发于荚膜组织胞浆菌的肉芽肿感染。该疾病的病理生理学基于纵隔重要器官结构被包裹在致密的纤维化肿块内。这个肿块似乎源于侵袭性慢性炎症过程,导致这些结构受到侵蚀和外部压迫。以下病例报告说明了这种疾病实体的多样性,代表了来自俄亥俄河谷地区(组织胞浆菌病的流行地区)的患者群体。本报告的目的是阐明硬化性纵隔炎的各种临床表现,并将病理过程与合理的治疗方法相关联。