Ludwikowska Kamila, Konieczna Karolina, Szarek Anna, Kustrzycka-Kratochwil Dorota, Sukiennik-Kujawa Małgorzata, Kalicińska Elżbieta, Banasiak Waldemar, Ponikowski Piotr, Jankowska Ewa A
Studenckie Koło Naukowe przy Klinice Chorób Serca.
Kardiol Pol. 2013;71(8):861-3. doi: 10.5603/KP.2013.0202.
Tetralogy of Fallot is the most common cyanotic congenital heart disease. Total surgical correction of this defect during infancyallows for long-term survival in most of the patients. The long-term prognosis for untreated tetralogy of Fallot is poor and patients who have not undergone total surgical repair rarely live to old age. We present a case of 67-year-old man with not corrected tetralogy of Fallot diagnosed at the age of 44 years without typical clinical symptoms.
法洛四联症是最常见的青紫型先天性心脏病。婴儿期对该缺陷进行完全手术矫正可使大多数患者长期存活。未经治疗的法洛四联症长期预后较差,未接受完全手术修复的患者很少活到老年。我们报告一例67岁男性患者,44岁时被诊断为未经矫正的法洛四联症,当时无典型临床症状。