Silver R M, Miller K S
Medical University of South Carolina, Charleston.
Rheum Dis Clin North Am. 1990 Feb;16(1):199-216.
The lungs are frequently affected in systemic sclerosis, and pulmonary disease may significantly influence morbidity and mortality. The clinical, radiographic, and physiologic features of scleroderma lung disease are discussed in this article, as are new approaches to the detection and study of interstitial pneumonitis. The pathogenesis of pulmonary fibrosis is discussed in the context of data derived from bronchoalveolar lavage studies. Pulmonary vascular disease and less common pulmonary features of systemic sclerosis are also discussed.
系统性硬化症常累及肺部，肺部疾病可能会显著影响发病率和死亡率。本文讨论了硬皮病肺部疾病的临床、影像学和生理学特征，以及间质性肺炎检测和研究的新方法。在支气管肺泡灌洗研究数据的背景下，讨论了肺纤维化的发病机制。还讨论了系统性硬化症的肺血管疾病和较少见的肺部特征。
