Inci Ilhan, Soltermann Alex, Schneiter Didier, Weder Walter
Department of Thoracic Surgery, University Hospital, Zurich, Switzerland
Department of Pathology, University Hospital, Zurich, Switzerland.
Eur J Cardiothorac Surg. 2014 Aug;46(2):331-2. doi: 10.1093/ejcts/ezt544. Epub 2013 Nov 25.
Malignant peripheral nerve sheath tumours (MPNSTs) may occur in any peripheral nerve. They are often found in the chest wall and the posterior mediastinum. On the other hand, primary pulmonary MPNST is extremely rare, and surgically treated cases have been reported. Here, we present 3 cases of primary MPNST originating from the pulmonary parenchyma who underwent surgery in our institution. We discuss the possible clinical and pathological associations in the view of the literature.
恶性外周神经鞘膜瘤（MPNSTs）可发生于任何外周神经。它们常出现在胸壁和后纵隔。另一方面，原发性肺MPNST极为罕见，已有手术治疗病例的报道。在此，我们呈现3例源自肺实质的原发性MPNST病例，这些病例在我们机构接受了手术。我们结合文献探讨可能的临床和病理关联。
