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播散性腹膜平滑肌瘤病伴腹水和子宫内膜异位症:一例报告并文献复习

Leiomyomatosis peritonealis disseminata associated with ascites and endometriosis: a case report and review of the literature.

作者信息

De Vos T, Weyers S, Braems G, Villeirs G, Lambein K, Makar A, Tummers Ph, Van Den Broecke R

机构信息

Ghent University Hospital, Women's Clinic, Ghent, Belgium.

出版信息

Acta Chir Belg. 2013 Sep-Oct;113(5):357-63.

PMID:24294802
Abstract

We present a case of leiomyomatosis peritonealis disseminata (LPD) and review the literature. LPD is a rare, benign disorder that is characterized by multiple subperitoneal or peritoneal nodules of varying sizes on the omentum and peritoneal surfaces, grossly resembling disseminated carcinoma. It should be differentiated from other peritoneal tumors. It is mostly asymptomatic and diagnosis is often incidental during surgery. One should be aware of the iatrogenic component of this entity. LPD is being documented with increasing frequency. We report the case of a 39-year-old woman with chronic abdominal pain and heavy dysmenorrhea due to endometriosis associated with LPD. She underwent an abdominal hysterectomy with bilateral salpingo-oophorectomy and omentectomy. LPD and endometriosis is a known association. LPD with ascites and endometriosis however has not yet been reported.

摘要

我们报告一例播散性腹膜平滑肌瘤病(LPD)并复习相关文献。LPD是一种罕见的良性疾病,其特征是在大网膜和腹膜表面有多个大小不一的腹膜下或腹膜结节,肉眼上很像播散性癌。它应与其他腹膜肿瘤相鉴别。其大多无症状,诊断常于手术中偶然发现。应注意该疾病存在医源性因素。LPD的报告频率越来越高。我们报告一例39岁女性,因与LPD相关的子宫内膜异位症而患有慢性腹痛和严重痛经。她接受了腹式子宫切除术、双侧输卵管卵巢切除术和大网膜切除术。LPD与子宫内膜异位症是一种已知的关联。然而,伴有腹水的LPD和子宫内膜异位症尚未见报道。

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