非致密型心肌病所致严重心力衰竭：一例报告

Severe heart failure due to noncompaction cardiomyopathy: a case report.

作者信息

Cantero-Pérez E M, Sobrino-Márquez J M, Adsuar-Gómez A, Lage-Gallé E, Grande-Trillo A, Martínez-Martínez A

机构信息

Department of Cardiology, Heart Area, Clinical Management Unit, Virgen del Rocío University Hospital, Seville, Spain.

出版信息

Transplant Proc. 2013;45(10):3672-4. doi: 10.1016/j.transproceed.2013.10.018.

DOI:10.1016/j.transproceed.2013.10.018

PMID:24314993

Abstract

Noncompaction cardiomyopathy involves an infrequent pathology whose diagnosis has been rising in recent years owing to a better understanding of the disease and, therefore, better diagnosis. Today, there are no well established protocols for its treatment. For this reason, it is necessary to adapt the therapy of choice to each patient. We report the case of a 35-year-old man with no past medical history of interest who was admitted due to acute pulmonary edema. Diagnostic tests revealed noncompaction cardiomyopathy with biventricular severe systolic dysfunction. In this situation, heart transplantation was considered to be the best therapeutic option, which was carried out with an uneventful postoperative course. This is one of the few cases reported in the literature for this issue.

摘要

致密化不全心肌病是一种罕见的病理状况，近年来由于对该疾病有了更深入的了解，进而诊断水平提高，其诊断率呈上升趋势。目前，对于该病尚无成熟的治疗方案。因此，有必要根据每位患者的情况调整首选治疗方法。我们报告了一例35岁男性患者，其既往无相关病史，因急性肺水肿入院。诊断检查显示为致密化不全心肌病伴双心室严重收缩功能障碍。在此情况下，心脏移植被认为是最佳治疗选择，并顺利完成了手术，术后病程平稳。这是文献中报道的关于此问题的少数病例之一。