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Intracranial fibromuscular dysplasia presenting as various ocular manifestations.

作者信息

Choi Jae-Hwan, Jung Jaeho, Park Kyung-Pil, Baik Seung Kuk, Choi Kyung Un, Choi Kwang-Dong, Choi Hee-Young, Shin Jong-Hoon

机构信息

Department of Neurology, Pusan National University School of Medicine, Research Institute for Convergence of Biomedical Science and Technology, Pusan National University Yangsan Hospital, Republic of Korea.

Department of Ophthalmology, Pusan National University School of Medicine, Research Institute for Convergence of Biomedical Science and Technology, Pusan National University Yangsan Hospital, Republic of Korea.

出版信息

J Neurol Sci. 2014 Feb 15;337(1-2):232-4. doi: 10.1016/j.jns.2013.12.009. Epub 2013 Dec 11.

Abstract

Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease that mainly affects renal, extracranial carotid, and vertebral arteries. Intracranial FMD is uncommon unlike extracranial or renal FMD, and the primary manifestation of intracranial FMD is intracranial aneurysm. We report an unusual case of intracranial FMD showing various ocular manifestations, including central retinal artery occlusion, transient monocular blindness, and oculomotor nerve palsy without renal involvement.

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