原发性纵隔血管外皮细胞瘤行术前栓塞和手术治疗。

Primary mediastinal hemangiopericytoma treated with preoperative embolization and surgery.

机构信息

Department of Surgical Oncology, Army Hospital (Research and Referral), Delhi, India.

出版信息

Ann Thorac Surg. 2014 Jan;97(1):335-8. doi: 10.1016/j.athoracsur.2013.04.128.

DOI:10.1016/j.athoracsur.2013.04.128

Abstract

Hemangiopericytomas are rare tumors originating from vascular pericytes. The mediastinum is an extremely uncommon site with only a few cases reported. Diagnosis is based on histopathology and immunohistochemistry, which differentiates them from synovial sarcoma and solitary fibrous histiocytoma. They have a variable malignant potential. Treatment is mainly surgical extirpation as the role of adjuvant therapy is controversial. Preoperative embolization has been sparingly used. We report a case of primary mediastinal hemangiopericytoma in a 47-year-old man treated successfully with preoperative embolization and surgery.

摘要

血管外皮细胞瘤起源于血管周细胞的罕见肿瘤。纵隔是一个非常罕见的部位，仅有少数病例报道。诊断基于组织病理学和免疫组织化学，这将它们与滑膜肉瘤和孤立性纤维性肿瘤区分开来。它们具有不同的恶性潜能。治疗主要是手术切除，因为辅助治疗的作用存在争议。术前栓塞术很少使用。我们报告了一例 47 岁男性原发性纵隔血管外皮细胞瘤，成功地进行了术前栓塞和手术治疗。