Department of Radio Diagnosis, Sree Balaji Medical College and Hospital, No 7 Works Road, Chrompet, Chennai, 600 044, Tamil Nadu, India.
Hernia. 2014 Jun;18(3):439-42. doi: 10.1007/s10029-014-1216-x. Epub 2014 Jan 12.
Obturator hernia is a very rare type of abdominal hernia which constitutes <1 % of all the hernias. It is an important cause of small bowel obstruction which is associated with a high mortality rate if left untreated. Obturator hernia typically occurs in an elderly women or patients with chronically raised intraabdominal pressure or previous multiple pregnancies. We report a case of obstructed obturator hernia in a young female patient with Marfan's syndrome complicated with dissecting aortic aneurysm and chronic kidney disease. Though recurrent and incisional hernia constitutes one of the minor diagnostic criteria of Marfan's syndrome, obturator hernia being a very rare entity, has been reported very rarely in a patient with Marfan's syndrome.
闭孔疝是一种非常罕见的腹外疝，占所有疝的<1%。它是小肠梗阻的一个重要原因，如果不治疗，死亡率很高。闭孔疝通常发生在老年女性或慢性腹腔内压升高或多次妊娠的患者中。我们报告了一例马凡氏综合征合并夹层主动脉瘤和慢性肾脏病的年轻女性患者的闭孔疝嵌顿。尽管复发性和切口疝是马凡氏综合征的次要诊断标准之一，但闭孔疝是一种非常罕见的疾病，在马凡氏综合征患者中很少有报道。
