George Sam Varghese, Samarasam Inian, Mathew George, Chandran Sudhakar
Christian Medical College and Hospital Vellore, Ida Scudder Road, Vellore, Tamil Nadu 632 004 India ; Department of Upper GI surgery, Department of surgery, Christian Medical College Vellore, Vellore, Tamil Nadu 632004 India.
Indian J Surg. 2013 Jun;75(Suppl 1):80-1. doi: 10.1007/s12262-011-0369-4. Epub 2011 Nov 11.
Rapunzel syndrome is an unusual and rare type of trichobezoar. Bezoars can be classified according to the primary constituent, as trichobezoar (hair), phytobezoar (plant material) or miscellaneous (pharmacobezoar, lactobezoar, fungal agglomeration and foreign bodies). When a long tail of hair strands extends from the main mass in the stomach along the small intestine and beyond it is known as Rapunzel syndrome. Here we are reporting a case of Rapunzel syndrome with a very long tail who was managed successfully. And reviewing the literature on the pathophysiology and management of these patients. These patients commonly present with obstructive symptoms and needs a high index of suspicion especially, in young female patients who have alopecia circumscripta and underlying psychiatric disorders. Early diagnosis and treatment is required to prevent complications due to this condition. Currently surgical management of this condition is the treatment of choice.
长发公主综合征是一种罕见的毛粪石类型。粪石可根据主要成分分类,如毛粪石(毛发)、植物粪石(植物材料)或其他(药物粪石、乳粪石、真菌团块和异物)。当一束长发从胃内的主要团块沿着小肠延伸并超出小肠时,就称为长发公主综合征。在此,我们报告一例具有极长尾巴的长发公主综合征病例,并成功进行了治疗。同时回顾了关于这些患者病理生理学和治疗的文献。这些患者通常表现为梗阻症状,尤其在患有局限性脱发和潜在精神疾病的年轻女性患者中需要高度怀疑。需要早期诊断和治疗以预防该疾病引起的并发症。目前,这种疾病的手术治疗是首选治疗方法。