Karbeet Radhakrishna Geeta, Bhat P R, Shenoy Rajgopal K, Pai Srinivas, Singh Harpreet
Department of Surgery, Kasturba Medical College Hospital, Manipal University, Manipal, Karnataka India 576104.
Indian J Surg. 2013 Jun;75(Suppl 1):131-3. doi: 10.1007/s12262-012-0515-7. Epub 2012 Jun 1.
Although fibromatosis of the mesentery is a very rare locally aggressive benign condition, the uncertain treatment modalities, the natural history of the disease, and the other common differential diagnosis of the condition along with inexperience of the general clinicians with this disease pose a challenge to the professionals. The prolonged periods of stability and even regression in size of the tumor offer a hope for treatment. Accounting for 0.03 % of all neoplasms, it is also known as deep fibromatosis and desmoid tumor. Here, we discuss one case of primary mesenteric fibromatosis in a young male patient who presented to us with chronic abdominal pain after he was treated for acid peptic disease for the same at a local hospital. This case shows how management of this disease can be delayed due to unfamiliarity among clinicians of this condition. In our patient, a palliative surgical management plan was undertaken due to symptomatic mass in the abdomen, owing to unresectability.
尽管肠系膜纤维瘤病是一种非常罕见的局部侵袭性良性疾病，但治疗方式不确定、疾病的自然史、该病症的其他常见鉴别诊断以及普通临床医生对这种疾病缺乏经验，给专业人员带来了挑战。肿瘤长时间保持稳定甚至体积缩小，为治疗带来了希望。它占所有肿瘤的0.03%，也被称为深部纤维瘤病和硬纤维瘤。在此，我们讨论一例年轻男性原发性肠系膜纤维瘤病病例，该患者在当地医院接受消化性溃疡疾病治疗后，因慢性腹痛前来就诊。该病例显示了由于临床医生对这种病症不熟悉，如何导致对该疾病的治疗延迟。在我们的患者中，由于腹部有症状性肿块且无法切除，因此采取了姑息性手术治疗方案。
