Shah Mushtaq, Azam Bushra
Castle Hill Hospital, Cottingham, UK.
Mcgill J Med. 2007 Jul;10(2):90-2.
Desmoid tumours are benign tumours originating from the musculoaponeurotic structures of the body. They are mainly composed of collagen. These tumours commonly occur in post-partum women in whom they originate from the rectus abominus and in old surgical incisions. Here we present a case report of a young gentleman who presented with an acute surgical abdomen and subsequently underwent a laparotomy and was found to have an inflammatory mass. Histological analysis of this mass revealed mesenteric fibromatosis (desmoid tumour). I wish to present this interesting case because the patient was neither female nor someone who had previously undergone any surgery. It is rare for mesenteric fibromatosis to present with intestinal perforation and only one case been reported in the literature thus far (1). An important learning point from this case is that rare pathology can manifest itself with common signs and symptoms.
硬纤维瘤是起源于身体肌膜结构的良性肿瘤。它们主要由胶原蛋白组成。这些肿瘤常见于产后女性，起源于腹直肌，也见于旧的手术切口处。在此，我们报告一例年轻男性病例，该患者因急腹症就诊，随后接受了剖腹手术，术中发现有一个炎性肿块。对该肿块的组织学分析显示为肠系膜纤维瘤病（硬纤维瘤）。我希望展示这个有趣的病例，因为患者既非女性，也未曾接受过任何手术。肠系膜纤维瘤病伴肠穿孔的情况罕见，迄今为止文献中仅报道过一例(1)。该病例的一个重要经验是，罕见的病理情况可能以常见的体征和症状表现出来。
