Bharati S, Swerdlow M A, Vitullo D, Chiemmongkoltip P, Lev M
Department of Pathology, Deborah Heart and Lung Center, Browns Mills, New Jersey 08015.
Pacing Clin Electrophysiol. 1987 Sep;10(5):1058-70. doi: 10.1111/j.1540-8159.1987.tb06125.x.
This is a case of a child with neonatal lupus and congenital atrioventricular (AV) block, born to a mother with asymptomatic, systemic lupus erythematosus (SLE). The child, despite pacemaker insertion, died of septicemia and myocarditis at the age of three months. Although the association of neonatal lupus with congenital AV block is well-recognized, there are only few pathologic studies of the conduction system reported in the literature. This is such a study in which we emphasize that, due to an altered immune system in the child, septicemia may be the cause of death in some cases.
这是一例患有新生儿狼疮和先天性房室传导阻滞的患儿病例，其母亲患有无症状系统性红斑狼疮（SLE）。该患儿尽管植入了起搏器，但仍在三个月大时死于败血症和心肌炎。虽然新生儿狼疮与先天性房室传导阻滞的关联已得到充分认识，但文献中报道的关于传导系统的病理研究却很少。本研究强调，由于患儿免疫系统改变，败血症在某些情况下可能是导致死亡的原因。
