Lourenço Cátia, Oliveira Nuno, Ramos Filomena, Ferreira Isabel, Oliveira Mário
Rev Bras Ginecol Obstet. 2013 Dec;35(12):575-82. doi: 10.1590/s0100-72032013001200008.
Aggressive angiomyxoma is a rare, slow-growing soft tissue tumor that usually arises in the pelvis and perineal regions of women in reproductive age, with a marked tendency to local recurrence. Because of its rarity, it is often initially misdiagnosed. Surgical resection is the main treatment modality of aggressive angiomyxoma. We describe a case of a vaginal aggressive angiomyxoma in a 47-year-old woman in which the diagnosis was only made after histological examination. The etiology, presentation, diagnosis and management of this rare tumor are outlined. Angiomyxoma of vulva and vagina refers to a rare disease. Pre-operative diagnosis is difficult due to rarity and absence of diagnostic features, but it should be considered in every mass in genital, perianal and pelvic region in a woman in the reproductive age. Thus, these cases should have complete radiological workup before excision, as pre-diagnosis can change the treatment modality and patient prognosis'.
侵袭性血管黏液瘤是一种罕见的、生长缓慢的软组织肿瘤，通常发生于育龄期女性的盆腔和会阴区域，具有明显的局部复发倾向。由于其罕见性，它常常在最初被误诊。手术切除是侵袭性血管黏液瘤的主要治疗方式。我们描述了一例47岁女性阴道侵袭性血管黏液瘤的病例，该病例仅在组织学检查后才得以确诊。本文概述了这种罕见肿瘤的病因、表现、诊断及治疗。外阴和阴道血管黏液瘤是一种罕见疾病。由于其罕见性及缺乏诊断特征，术前诊断困难，但对于育龄期女性生殖器、肛周和盆腔区域的每个肿块都应考虑到该病。因此，这些病例在切除前应进行全面的影像学检查，因为术前诊断可能会改变治疗方式和患者预后。
