[主动脉供血型肺囊性发育不良的诊断与外科治疗]

[Diagnosis and surgical treatment of cystic pulmonary hypoplasia with aortic blood supply].

作者信息

Opanasenko N S, Klimenko V I, Kshanovskiĭ A É, Tereshkovich A V, Kalenichenko M I, Konik B N, Demus R S, Obremskaia O K, Levanda L I, Kononenko V A, Mikitenko I Iu

出版信息

Klin Khir. 2013 Dec(12):44-8.

PMID:24502010

Abstract

Cystic pulmonary hypoplasia with aortic blood supply--it is a rare inborn failure, in which the part of pulmonary tissue is developing separately from tracheo-bronchial tree and takes blood supply from systemic blood circulation. Diagnosis of the disease is a complicated, and it is necessary to apply modern radiological methods of visualization. The results of treatment of 27 patients, suffering cystic pulmonary hypoplasia with aortic blood supply, in the clinic through 50 yrs, were analyzed. All the patients were operated on.In 17 (63%) patients lobectomy was performed, in 4 (14.8%)--the left-sided lower lobe pyramid was excised, in 1 (3.7%)--the left-sided wedge resection of C(X), in 1 (3.7%)--the left-sided pulmonectomy, in 1 (3.7%)--left-sided resection of C(VIII) - C(IX). The rate of intraoperative complications--14.8%, and postoperative--7.4%. Efficacy of surgical treatment for this period constitutes 100%.

摘要

伴有主动脉供血的囊性肺发育不全——这是一种罕见的先天性疾病，其中部分肺组织与气管支气管树分离发育，并从体循环获取血液供应。该疾病的诊断较为复杂，需要应用现代影像学可视化方法。对50年间在该诊所接受治疗的27例伴有主动脉供血的囊性肺发育不全患者的治疗结果进行了分析。所有患者均接受了手术。17例（63%）患者进行了肺叶切除术，4例（14.8%）——切除了左侧下叶锥体，1例（3.7%）——对C(X)进行了左侧楔形切除术，1例（3.7%）——进行了左侧全肺切除术，1例（3.7%）——切除了左侧C(VIII)-C(IX)。术中并发症发生率为14.8%，术后为7.4%。这一时期手术治疗的有效率为100%。