Martini Joyce, Voos Mariana Callil, Hukuda Michele Emy, Resende Maria Bernadete Dutra de, Caromano Fátima Aparecida
Laboratório de Fisioterapia e Comportamento, Faculdade de Medicina, Universidade de São Paulo, Sao PauloSP, Brazil.
Hospital das Clínicas, Faculdade de Medicina, Universidade de São Paulo, Sao PauloSP, Brazil.
Arq Neuropsiquiatr. 2014 Jan;72(1):5-11. doi: 10.1590/0004-282X20130196.
During the transitional phase (ambulatory to non-ambulatory), synergies characterize the evolution of Duchenne muscular dystrophy (DMD). This study was performed to describe and quantify compensatory movements while sitting down on/rising from the floor and climbing up/down steps.
Eighty videos (5 children × 4 assessments × 4 tasks) were recorded quarterly in the year prior to gait loss. Compensatory movements from the videos were registered based on the Functional Evaluation Scale for DMD.
The most frequently observed compensatory movements were upper limb support on lower limbs/floor/handrail during all the tasks and lumbar hyperlordosis, trunk support on handrail, equinus foot, increased base of support, non-alternated descent, and pauses while climbing up/down steps.
Climbing up/down steps showed a higher number of compensatory movements than sitting down on/rising from the floor, which seemed to be lost before climbing up/down steps in ambulatory children with DMD.
在过渡阶段（从能行走至不能行走），协同作用是杜氏肌营养不良症（DMD）病情发展的特征。本研究旨在描述和量化在从地面坐下/起身以及上下楼梯时的代偿性动作。
在步态丧失前一年，每季度记录80段视频（5名儿童×4次评估×4项任务）。根据DMD功能评估量表记录视频中的代偿性动作。
在所有任务中，最常观察到的代偿性动作是上肢支撑下肢/地面/扶手、腰椎前凸增加、躯干支撑扶手、马蹄足、支撑面增大、非交替下降以及上下楼梯时的停顿。
上下楼梯时出现的代偿性动作比从地面坐下/起身时更多，在能行走的DMD儿童中，这些代偿性动作似乎在上下楼梯之前就已消失。
