Pal Kamalesh
Division of Pediatric Surgery, Department of Surgery,King Fahad Hospital of the University, College of Medicine, University of Dammam, Al Khobar 31952, Kingdom of Saudi Arabia.
Afr J Paediatr Surg. 2014 Jan-Mar;11(1):74-6. doi: 10.4103/0189-6725.129241.
Congenital hernia of the umbilical cord (CHUC) is a rare congenital entity compared to more common post-natally occurring umbilical hernia. Although recognized as a distinct entity since 1920s, CHUC is often misdiagnosed as a small omphalocele, resulting in its underreporting. We present the first case report of CHUC associated with extracelomic colonic atresia, complicated by perinatal perforation in a newborn. We also discuss the differentiating features from other anterior abdominal wall defects such as omphalocele and gastroschisis including its embryogenesis.
与更常见的出生后发生的脐疝相比，先天性脐带疝（CHUC）是一种罕见的先天性疾病。尽管自20世纪20年代以来就被确认为一种独特的疾病，但CHUC常被误诊为小型脐膨出，导致报告不足。我们报告了首例与腹腔外结肠闭锁相关的CHUC病例，该病例在新生儿期并发围产期穿孔。我们还讨论了CHUC与其他前腹壁缺损（如脐膨出和腹裂）的鉴别特征，包括其胚胎发生。
