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气管的上皮-肌上皮癌——一种罕见实体病例报告。

Epithelial-myoepithelial carcinoma of the trachea-a rare entity case report.

机构信息

1 Intesive Care Unit, 2 Pathology Department, "G. Papanikolaou" General Hospital, Thessaloniki, Greece ; 3 Pulmonary Department, 4 Cardiothoracic Surgery Department, "G. Papanikolaou" General Hospital, Aristotle University of Thessaloniki, Thessaloniki, Greece ; 5 Oncology Department, "Saint" Luke Private Hospital, Thessaloniki, Greece ; 6 Anesthesiology Department, "Saint" Luke Private Hospital, Thessaloniki, Greece ; 7 Anesthesiology Department, University Hospital of Larisa, Greece.

出版信息

J Thorac Dis. 2014 Mar;6 Suppl 1(Suppl 1):S194-9. doi: 10.3978/j.issn.2072-1439.2013.11.17.

Abstract

Epithelial-myoepithelial tumors of the lung are rare neoplasms whose biological behavior and clinical course still remain to be defined. Epithelial-myoepithelial carcinoma (EMCa) is a low-grade malignant tumour. According to literature, most commonly occurs in salivary glands, particularly in parotic gland, but it can also occur in unusual locations such as breast, lachrymal gland, nose, paranasal sinus, lung, bronchus and, as in our case, trachea. There are no many documented case reports of a primary myoepithelial carcinoma in the trachea. We report a case of a 34-year-old man diagnosed with this unusual location of an epithelial-myoepithelial tumor. The tumour was removed by segmental tracheal resection and end-to-end anastomosis.

摘要

肺上皮-肌上皮肿瘤是一种罕见的肿瘤,其生物学行为和临床过程仍有待确定。上皮-肌上皮癌(EMCa)是一种低级别恶性肿瘤。根据文献记载,最常见于唾液腺,特别是腮腺,但也可发生于不常见的部位,如乳腺、泪腺、鼻、副鼻窦、肺、支气管,以及在我们的病例中,气管。气管内原发性肌上皮癌的病例报告并不多。我们报告了一例 34 岁男性患者,诊断为这种不常见部位的上皮-肌上皮肿瘤。肿瘤通过节段性气管切除术和端端吻合术切除。

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本文引用的文献

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[Epithelial-myoepithelial carcinoma of the trachea. Case report and review of the literature].
Pathologe. 2013 Feb;34(1):56-64. doi: 10.1007/s00292-012-1610-z.

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